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We present the case of a patient with Cushing's syndrome secondary to ectopic ACTH secretion. A MR of the head showed a left-sided nasal mass extending down from the cribriform plate. The patient underwent endoscopic resection with nearly complete removal of the mass. Histological examination showed an ACTH-secreting olfactory neuroblastoma (ONB). The patient's cortisol levels returned to normal range after surgery and have remained normal for over a year. ONB is a rare cause for ectopic ACTH secretion. This case highlights the diagnostic and management difficulties in patients with ectopic ACTH secretion, and provides a brief review of ONB.

Original publication

DOI

10.1007/s00701-017-3447-y

Type

Journal article

Journal

Acta Neurochir (Wien)

Publication Date

05/2018

Volume

160

Pages

1023 - 1026

Keywords

ACTH, Cushing’s, Ectopic, Olfactory neuroblastoma, Cushing Syndrome, Esthesioneuroblastoma, Olfactory, Humans, Male, Middle Aged, Nose Neoplasms